All::Respiratory::Diseases::Kartagener's syndrome

Intro

What are the main clinical features of Kartagener's syndrome?

  • dextrocardia or complete situs inversus
  • bronchiectasis
  • recurrent sinusitis
  • subfertility (secondary to diminished sperm motility and defective ciliary action in the fallopian tubes)

What is the pathophysiology of Kartagener's syndrome?

dynein arm defect results in immotile cilia